agranulocytosis, infantile genetic

agranulocytosis, infantile genetic An inherited condition characterized by a lack of granulocytes (neutrophils), a type of white blood cell that is important in fighting infection, and a predisposition to frequent bacterial infections. Also known as Kostmann disease or syndrome and genetic infantile agranulocytosis. See also agranulocytosis; granulocytopenia; severe congenital neutropenia.